Lipodystrophia centrifugalis abdominalis infantilis(LCAI), an atypical form of progressive lipodystrophy, is a disease named by Imamura et al in 1971, and reported a few cases in Japan. We report a case who has been diagnosed as LCAI.
The patient is 5 and half year old boy. He had 2cm by 7cm sized, linear depressed lesion with surrounding erythema on the right inguinal region which was noticed 5 months prior to first diagnosis. There was no family history, no physical abnormality. except skin lesion.
Complete blood cell count, urinalysis, stool examination, liver function test and chest X-ray were within normal limit. Biopsy specimens from the depressed lesion and surrounding erythematous area revealed slight atrophy of the epidermis, a mild lymphocyte infiltration around the vessels and eccrine glands in the upper part of dermis, markedly decreased amount of subcutaneous adipose tissue with mild lymphocyte infiltration in depressed area and marked lymphocyte infiltration, intermingled with histiocyte in surrounding erythematous area, but normal amount of adipose tissue.
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